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封面摄影：邓敏兴老师 A 58-year-old man presented to our hospital with cerebellar ataxia, pyramidal signs, dysarthria, bilateral deafness, and cognitive impairment. 一名58岁男子因小脑性共济失调，锥体束征，构音障碍，双侧耳聋，认知障碍来到我院。 These symptoms were consistent with superficial siderosis(SS) of the CNS, confirmed by MRI (figureA). 这些症状与中枢神经系统表面铁沉积症一致，经MRI证实(图A)。 Axial T2-weighted gradient echo MRI shows hemosiderin deposition in supratentorial brain (inside of sulcus) and in infratentorial brain (on the surface of the brainstem and the cerebellum). 轴位t2加权梯度回波MRI显示幕上(脑沟内)和幕下(脑干和小脑表面)含铁血黄素沉积。 Cerebral angiography showed a dural arterio-venous fistula perispinal and pontic with venous drainage in the left foramen C1-C2, fed by meningeal branches of the vertebral artery (figure, B).The fistulous point was clipped. 脑血管造影示硬脑膜动静脉瘘，脊髓周围及桥脑的引流静脉在左侧枕骨大孔C1-C2水平，由椎动脉脑膜支供血(图B)。瘘管尖被夹闭了。 Cerebral angiography: dural arteriovenous fistula in the C1-C2 left foramen, fed by meningeal branches of the vertebral artery. 脑血管造影:硬脑膜动静脉瘘在左侧枕骨大孔C1-C2水平，由椎动脉的脑膜分支供血。 SS of CNS is a rare disease resulting from hemosiderin deposition on the surface of the CNS and cranial nerves.At diagnosis, the etiology may not be known. Finding etiology is necessary (trauma, vascular malformation). 中枢神经系统表面铁沉积症为一种罕见的疾病，由于含铁血黄素沉积在中枢神经系统和颅神经的表面。在诊断时，病因可能不是已知的。必须找到病因(外伤、血管畸形)。 小神经联盟 小神经联盟 |
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